Retinal vasculitis associated with CREST syndrome.

Laura Kopplin // Publications // Jun 01 2018

PubMed ID: 29780934

Author(s): Yang S, Kopplin LJ, Rosenbaum JT. Retinal vasculitis associated with CREST syndrome. Am J Ophthalmol Case Rep. 2018 Mar 2;10:185-188. doi: 10.1016/j.ajoc.2018.02.022. eCollection 2018 Jun. PMID 29780934

Journal: American Journal Of Ophthalmology Case Reports, Volume 10, Jun 2018

PURPOSE To report two cases of retinal vasculitis associated with CREST syndrome, a novel ocular finding.

OBSERVATIONS We report two cases of patients with CREST syndrome with ocular inflammatory disease. Patient 1 presented with a right unilateral panuveitis with extensive retinal vasculitis and evidence of prior uveitis in the contralateral eye. Patient 2 presented with a left branch retinal artery occlusion and bilateral retinal vasculitis. Both patients underwent treatment with prednisone and mycophenolate motefil.

CONCLUSIONS AND IMPORTANCE Retinal vasculitis has not been previously reported in CREST syndrome. Prompt therapy with immunomodulatory therapy can potentially minimize ocular morbidity.