Melanotic neuroectodermal tumor of infancy (retinal anlage tumor).

Daniel Albert // Publications // Jan 01 1985

PubMed ID: 2983280

Author(s): Lamping KA, Albert DM, Lack E, Dickersin GR, Chapman PH, Walton DS. Melanotic neuroectodermal tumor of infancy (retinal anlage tumor). Ophthalmology. 1985 Jan;92(1):143-9. PMID 2983280

Journal: Ophthalmology, Volume 92, Issue 1, Jan 1985

Six cases of the melanotic neuroectodermal tumor of infancy, including light and electron microscopic findings, are presented. The tumor, now believed to originate from neural crest, is usually cured by wide excision; however, malignant cases have been reported. Histopathologically, this lesion resembles neural retina and retinal pigment epithelium. It may involve the orbit but most frequently occurs in the maxilla. One case presented involved the orbit, another the anterior fontanelle, and four presented in the maxilla.